Crimean-Congo Hemorrhagic Fever in Humanized Mice Reveals Glial Cells as Primary Targets of Neurological Infection.
Document Type
Article
Publication Date
12-12-2017
JAX Location
Reprint Collection
JAX Source
J Infect Dis 2017 Dec 12; 216(11):1386-1397
Volume
216
Issue
11
First Page
1386
Last Page
1397
ISSN
1537-6613
PMID
28482001
DOI
https://doi.org/10.1093/infdis/jix215
Abstract
Crimean-Congo hemorrhagic fever (CCHF) is a tick-borne viral hemorrhagic disease seen exclusively in humans. Central nervous system (CNS) infection and neurological involvement have also been reported in CCHF. In the current study, we inoculated NSG-SGM3 mice engrafted with human hematopoietic CD34+ stem cells with low-passage CCHF virus strains isolated from human patients. In humanized mice, lethal disease develops, characterized by histopathological change in the liver and brain. To date, targets of neurological infection and disease have not been investigated in CCHF. CNS disease in humanized mice was characterized by gliosis, meningitis, and meningoencephalitis, and glial cells were identified as principal targets of infection. Humanized mice represent a novel lethal model for studies of CCHF countermeasures, and CCHF-associated CNS disease. Our data suggest a role for astrocyte dysfunction in neurological disease and identify key regions of infection in the CNS for future investigations of CCHF. J Infect Dis 2017 Dec 12; 216(11):1386-1397.
Recommended Citation
Spengler J,
Kelly Keating M,
McElroy A,
Zivcec M,
Coleman-McCray J,
Harmon J,
Bollweg B,
Goldsmith C,
Bergeron É,
Keck JG,
Zaki S,
Nichol S,
Spiropoulou C.
Crimean-Congo Hemorrhagic Fever in Humanized Mice Reveals Glial Cells as Primary Targets of Neurological Infection. J Infect Dis 2017 Dec 12; 216(11):1386-1397